OnCo
drugsProductApproved2025

Dordaviprone

Dordaviprone is the first drug ever approved for a lethal childhood and young-adult brain tumour, diffuse midline glioma with the H3 K27M mutation (August 2025).

FDA accelerated approval 6 August 2025 for patients ≥1 year with H3 K27M-mutant diffuse midline glioma progressing after prior therapy, based on an integrated analysis of 50 patients across five trials: ORR 22%, median duration of response 10.3 months. Brain-penetrant oral agent from Oncoceutics → Chimerix → Jazz Pharmaceuticals (2025). Confirmatory phase 3 ACTION trial (newly diagnosed, after radiotherapy) ongoing. Debate continues on the strength of single-arm evidence.

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Dordaviprone (ONC201)
PubChem
Modality
Small-molecule imipridone (ClpP agonist / DRD2 antagonist)
Mechanism
Hyperactivates the mitochondrial protease ClpP and antagonises dopamine receptor D2, triggering integrated stress response and apoptosis in H3 K27M-altered cells.
Brand / code
Modeyso · ONC201
Not appraisedSearch NICE
Notes
No UK marketing authorisation as of September 2026, so no NICE appraisal. Access only through a clinical trial or a company early access scheme.
NHS England
Not routinely funded

Sources: NICE search: dordaviprone. Funding decisions are indication-specific and change monthly; verify with NICE and your treating team.

Regulatory

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Approvals

RegionYearIndication
US2025Recurrent H3 K27M-mutant diffuse midline glioma, age ≥1 (accelerated)

Trials

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ClinicalTrials.gov · phase 2/3
refreshed 2026-09-09
6 studies2 recruiting4 Phase 22 Phase 3
Search “Dordaviprone” on ClinicalTrials.gov →
Counts are from a name search and may include unrelated studies; up to 100 studies are summarised.

Recruiting now (live from ClinicalTrials.gov)

Recruiting trials near you · live from ClinicalTrials.gov
Dordaviprone
intervention: Dordaviprone
Open on ClinicalTrials.gov →

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Latest papers

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Literature trend47 papers in the last 12 months-6% vs prior 12How this is computed
Latest papers · live from Europe PMC
Open in Europe PMC

Query for this drug: (TITLE:"Dordaviprone" OR ABSTRACT:"Dordaviprone" OR TITLE:"Modeyso" OR ABSTRACT:"Modeyso" OR TITLE:"ONC201" OR ABSTRACT:"ONC201") AND (cancer OR tumor OR tumour OR oncology OR carcinoma OR lymphoma OR leukemia OR leukaemia OR myeloma OR sarcoma OR melanoma OR glioma). Results are unfiltered search hits about Dordaviprone, not a curated reading list.

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